Perivascular epithelioid cell tumours (PEComas) are a family of rare mesenchymal tumours with discrete histologic and immunohistochemical characteristics. Even rarer among them are cutaneous and subcutaneous PEComas. We describe a 34-year-old lady presented with a large anterior abdominal subcutaneous lesion showing intact overlying skin and no obvious invasion of abdominal musculature. A wide local excision was performed. Histopathology revealed a solitary tumour measuring 75 x 55 x 90 mm with epithelioid cells in nests with thin fibrovascular septa and spindle cells. Resection margins were clear with no invasion to skin or rectus sheath. Tumour cells were only positive for HMB-45 but negative for other markers. This is the largest subcutaneous PEComas reported to date.
Perivascular epithelioid cell tumours (PEComas) are a family of rare mesenchymal tumours with discrete histologic and immunohistochemical characteristics. Even rarer among them are cutaneous and subcutaneous PEComas. We describe a 34-year-old lady presented with a large anterior abdominal subcutaneo...
مادة فرعية
Oman Medical Journal = المجلة الطبية العمانية